Page 21 - Delaware Medical Journal - January 2018

CASE REPORT
FIGURE 1
Axial HRCT images show bilateral and asymmetric pericochlear ring-like hypoattenuation (arrows), more extensive in the right middle ear.
FIGURE 2
CLINICAL PRESENTATION
Here the authors present a 68-year-old female with a long- standing history of bilateral cochlear otosclerosis. She initially underwent stapedectomy on the right ear at age 16 followed
by left sided stapedectomy at age 18. Despite these surgeries, the patient’s hearing continued to deteriorate, eventually resulting incomplete right-sided hearing loss by age 62. Word
discrimination in her left ear declined to 40 percent by age 66, which made her hearing aid only marginally useful. Hearing discrimination for loud speech (70 dB) with a hearing aid was
0 percent in the right ear while using sentences in quiet was
53 percent in the left ear. In 2015, she underwent cochlear implantation of a nucleus 512 device in her non-hearing right ear. A stiff styletted electrode was used to overcome obstructions
in the cochlea. Although only partial electrode insertion was possible due to the extent of her disease, she did experience a
Axial MR images of the skull base show strong pericochlear hypointensity
on heavily T2-weighted images and mild enhancement on gadolinium- enhanced images.
Del Med J | January 2018 | Vol. 90 | No. 1
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